Case Report | |||||
Dementia and Neurocognitive Disorders 2010: 9: 3: 100-102 | |||||
국소성 근긴장 이상이 초기 증상으로 발현된 크로이츠펠트-야콥 병 | |||||
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Jihoon Kim, M.D.*, Kee Ook Lee, M.D.*,† | |||||
Department of Neurology*, Konyang University College of Medicine, Daejeon; Department of Neurology†, Yonsei University College of Medicine, Seoul, Korea |
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Focal Dystonia as an Initial Manifestation of Sporadic | |||||
Jihoon Kim, M.D.*, Kee Ook Lee, M.D.*,† | |||||
Department of Neurology*, Konyang University College of Medicine, Daejeon; Department of Neurology†, Yonsei University College of Medicine, Seoul, Korea |
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Sporadic Creutzfeldt-Jakob disease (CJD) is a rare progressive spongiform encephalopathy. Involuntary movements commonly occur in the course of sporadic CJD, but focal dystonia alone as an initial manifestation is rare. We described a 40-yr-old man who presented with a 2 week history of focal dystonia in the neck and left arm. Interestingly, diffusion-weighted images revealed high signal intensities in the right temporal, posterior parietal, and occipital cortices rather than in the striatum. | |||||
Key Words: Creutzfeldt-Jakob disease, Dystonia, Magnetic resonance image | |||||